Differential diagnostic features between congenital haemangioma, KHE, and congenital fibrosarcoma: a single-centre experience
AbouZeid, Amr Abdelhamid; Mohammad, Shaimaa Abdelsattar; Aly, Nihal Hussein; Elghandour, Mostafa Mohamed; AbdelLatif, Mohamed; Elsayed, Safa Matbouly; El-Naggar, Osama; Attia, Enas A S; Ragab, Iman A;
Abstract
Congenital haemangioma (CH) is a rare benign vascular tumour presenting at birth with excellent prognosis. Usually, CH regresses without treatment within the first few months of life. Kaposiform Haemangioendothelioma (KHE) is another type of vascular tumours that has been described as benign with locally aggressive potential. Although the diagnosis of vascular tumours is usually straightforward based on typical clinical presentation, yet some confusing similarities may exist with congenital sarcomas.Conclusion: Data of cases managed at the vascular anomaly clinic during the period 2015 through 2019 were retrospectively analysed. The study included three groups of patients: cases diagnosed as congenital haemangioma (9 cases), cases of Kaposiform Haemangioendothelioma who presented in the neonatal period (7 cases), as well as cases of congenital fibrosarcoma (4 cases) that were referred to the vascular anomaly clinic because of apparent similarity with vascular tumours. The hallmark of the study was to compare clinical and imaging features in the three groups to facilitate differentiation and remove diagnostic confusion when managing these rare cases in the future. What is Known: • Congenital haemangioma is a rare benign vascular tumour presenting at birth. • Kaposiform Haemangioendothelioma is another type of vascular tumours that has been described as benign with locally aggressive potential. What is New: • Confusing similarities may exist between vascular tumours and congenital sarcomas.
Other data
Title | Differential diagnostic features between congenital haemangioma, KHE, and congenital fibrosarcoma: a single-centre experience | Authors | AbouZeid, Amr Abdelhamid ; Mohammad, Shaimaa Abdelsattar; Aly, Nihal Hussein; Elghandour, Mostafa Mohamed; AbdelLatif, Mohamed; Elsayed, Safa Matbouly; El-Naggar, Osama; Attia, Enas A S; Ragab, Iman A | Keywords | Fibrosarcoma; Hemangioma; Kaposiform haemangioendothelioma; Vascular tumours | Issue Date | 19-May-2021 | Journal | European journal of pediatrics | Volume | 180 | Start page | 2581 | End page | 2589 | ISSN | 0340-6199 1432-1076 |
DOI | 10.1007/s00431-021-04119-7 | PubMed ID | 34009469 |
Recommend this item
Similar Items from Core Recommender Database
Items in Ain Shams Scholar are protected by copyright, with all rights reserved, unless otherwise indicated.